Myeloid Sarcoma, a Rarity of the Head and Neck Region - A Case Report


Myeloid sarcoma
Acute myeloid leukemia
Lymphoid hypertrophy


How to Cite

Krishnamoorthy M, Lee BS, Binti Adzman S, Bin Hitam S. Myeloid Sarcoma, a Rarity of the Head and Neck Region - A Case Report. Integr J Med Sci [Internet]. 2017 Feb. 3 [cited 2022 Dec. 6];4. Available from:


Myeloid sarcoma is a rare disease, where a mass (tumor) of either myeloblasts or immature myeloid cells conglomerate in extramedullary anatomic sites. It may arise de-novo or it may present in association with acute myeloid leukemia. It can also occur in patients with myelodysplastic syndromes, myeloproliferative disorders, and blast transformation in myeloproliferative neoplasia. Myeloid sarcoma of the head and neck area can pose a diagnostic challenge because of the low frequency of occurrence, and the vast diversity of tumors occurring from multiple lineages in this anatomic region. This can lead to a broad spectrum of various differential diagnoses. Therefore, a high index of suspicion is required when dealing with a possible case of myeloid sarcoma, as it is a time-sensitive diagnosis with various diagnostic dilemmas. Here, we report an example, a case of tonsillar myeloid sarcoma. We wish to highlight the investigations that helped us procure this diagnosis in a timely manner.


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Copyright (c) 2017 Madhusudhan Krishnamoorthy et al.


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